Aortic valve avulsion after proximal aortic dissection in the Marfan syndrome: Echocardiographic features and management

Abstract

The cardiovascular complications of the Marfan syndrome are principally responsible for the reduced life expectancy of patients with this disorder. Aneurysmal dilatation of the aortic root leads to progressive aortic regurgitation and predisposes to aortic rupture. Dissection of the proximal aorta and aneurysmal tears without dissection are also recognised. Recent surgical approaches to aortic root aneurysm in this syndrome have recommended replacement of the ascending aorta and aortic valve with coronary reimplantation. Conservation of the aortic valve would offer several long-term advantages.