History and diagnosis

Abstract

Behçet's syndrome, named after Hulusi Behçet Professor of Dermatology in Istanbul who described the triple symptom complex in 1937, is a multisystem, immunologically medicated vasculopathy. The principal clinical features are orogenital aphthous ulceration, uveitis, with or without hypopyon and retinal vasculitis and skin lesions including erythema nodosum and acneiform pustules. Inflammatory arthritis, arterial and venous occlusion and arterial aneurysms, gastrointestinal and neurological lesions also occur. © 2010 Springer Science+Business Media, LLC.