Abstract
Connective tissue surrounds, supports, and connects a multitude of tissues and organs. It is composed of a cellular component (mostly fibroblasts) and extracellular matrix, with the latter consisting of fibers (collagen, elastic fibrils, etc.) and amorphous glycoproteins. Rare genetic defects in key connective tissue components lead to a heterogeneous group of diseases with multisystem involvement, called heritable connective tissue disorders.
Author supplied keywords
Cite
CITATION STYLE
Verstraeten, A., & Loeys, B. (2019). Clinical Aspects of Heritable Connective Tissue Disorders. In Surgical Management of Aortic Pathology: Current Fundamentals for the Clinical Management of Aortic Disease (pp. 523–530). Springer International Publishing. https://doi.org/10.1007/978-3-7091-4874-7_34
Register to see more suggestions
Mendeley helps you to discover research relevant for your work.
